Prion diseases

{
  "id": "MLC-T-AGR-005173",
  "term": "Prion diseases",
  "field": "Agriculture and food",
  "definition": "A group of genetic, infectious, or sporadic degenerative human and animal nervous system disorders associated with abnormal prions. In humans, these conditions generally feature dementia, ataxia, and a fatal outcome. Diseases in this category include Creutzfeldt-Jakob Syndrome; scrapie; bovine spongiform encephalopathy; chronic wasting disease of mule deer and elk; and transmissible mink encephalopathy. Pathologic features include a spongiform encephalopathy without evidence of inflammation.",
  "synonyms": [
    "TSE (transmissible spongiform encephalopathies)",
    "spongiform encephalopathies",
    "subacute spongiform encephalopathy",
    "subacute transmissible spongiform encephalopathies",
    "transmissible spongiform encephalopathies"
  ],
  "subject": "Animals, Livestock, One Health",
  "see_also": [
    "infectious diseases",
    "nervous system diseases",
    "prions",
    "PrPSc proteins",
    "foodborne illness",
    "bovine spongiform encephalopathy",
    "Creutzfeldt-Jakob Syndrome",
    "chronic wasting disease",
    "scrapie",
    "kuru",
    "transmissible mink encephalopathy"
  ],
  "references": [
    "NAL Agricultural Thesaurus and Glossary"
  ],
  "translations": {
    "es": "enfermedades por prión"
  },
  "url": "https://mlchart.com/terminology/agriculture/prion-diseases/"
}