MLchartDataset catalogue

hereditary paraganglioma-pheochromocytoma syndrome

Term · Oncology and biomedicine · MLC-T-ONC-003851

A rare, genetic disorder marked by tumors called paragangliomas, which are found in paraganglia. Paraganglia are groups of nerve-like cells found near the adrenal glands and near blood vessels or nerves in the head, neck, chest, abdomen, and pelvis. Paragangliomas that form in the adrenal glands are called pheochromocytomas. Paragangliomas are usually benign (not cancer), but sometimes become malignant (cancerous). People with hereditary paraganglioma-pheochromocytoma syndrome usually have more than one paraganglioma, and may have an increased risk of certain types of cancer, such as kidney cancer and thyroid cancer.

Table 1. Record
IdentifierMLC-T-ONC-003851
FieldOncology and biomedicine
ReferencesNCI Dictionary of Cancer Terms
Record as JSON
{
  "id": "MLC-T-ONC-003851",
  "term": "hereditary paraganglioma-pheochromocytoma syndrome",
  "field": "Oncology and biomedicine",
  "definition": "A rare, genetic disorder marked by tumors called paragangliomas, which are found in paraganglia. Paraganglia are groups of nerve-like cells found near the adrenal glands and near blood vessels or nerves in the head, neck, chest, abdomen, and pelvis. Paragangliomas that form in the adrenal glands are called pheochromocytomas. Paragangliomas are usually benign (not cancer), but sometimes become malignant (cancerous). People with hereditary paraganglioma-pheochromocytoma syndrome usually have more than one paraganglioma, and may have an increased risk of certain types of cancer, such as kidney cancer and thyroid cancer.",
  "references": [
    "NCI Dictionary of Cancer Terms"
  ],
  "url": "https://mlchart.com/terminology/oncology/hereditary-paraganglioma-pheochromocytoma-syndrome/"
}

Record 8,453 of 17,721 in Oncology and biomedicine terminology (MLC-0111). Request the full dataset.