MLchartDataset catalogue

Primary myelofibrosis

Term · Oncology and biomedicine · MLC-T-ONC-006918

A progressive, chronic disease in which the bone marrow is replaced by fibrous tissue and blood is made in organs such as the liver and the spleen, instead of in the bone marrow. This disease is marked by an enlarged spleen and progressive anemia. Also called agnogenic myeloid metaplasia, chronic idiopathic myelofibrosis, idiopathic myelofibrosis, and myelosclerosis with myeloid metaplasia.

Table 1. Record
IdentifierMLC-T-ONC-006918
FieldOncology and biomedicine
Synonymsagnogenic myeloid metaplasia; chronic idiopathic myelofibrosis; idiopathic myelofibrosis; myelosclerosis with myeloid metaplasia
ReferencesNCI Dictionary of Cancer Terms
Record as JSON
{
  "id": "MLC-T-ONC-006918",
  "term": "Primary myelofibrosis",
  "field": "Oncology and biomedicine",
  "definition": "A progressive, chronic disease in which the bone marrow is replaced by fibrous tissue and blood is made in organs such as the liver and the spleen, instead of in the bone marrow. This disease is marked by an enlarged spleen and progressive anemia. Also called agnogenic myeloid metaplasia, chronic idiopathic myelofibrosis, idiopathic myelofibrosis, and myelosclerosis with myeloid metaplasia.",
  "synonyms": [
    "agnogenic myeloid metaplasia",
    "chronic idiopathic myelofibrosis",
    "idiopathic myelofibrosis",
    "myelosclerosis with myeloid metaplasia"
  ],
  "references": [
    "NCI Dictionary of Cancer Terms"
  ],
  "url": "https://mlchart.com/terminology/oncology/primary-myelofibrosis/"
}

Record 13,620 of 17,717 in Oncology and biomedicine terminology (MLC-0111). Request the full dataset.